Giant Malignant Peripheral Nerve Sheath Tumor of Scalp in Non-neurofibromatosis Person: A Rare Case Report
نویسندگان
چکیده
Malignant peripheral nerve sheath tumors (MPNSTs) are rare neoplasms with an incidence of about 0.001% in general population. They usually arise from components of nerve sheath such as perineural fibroblasts or Schwann cells, and are often considered as a form of soft tissue sarcoma.1 Most of these MPNSTs are located in the buttocks, thighs, brachial plexus, and paraspinal region, and are rarely seen in the head and neck. Only few cases of primary scalp MPNST have been reported till date.2,3 This article describes a rare case report of MPNSTof the occipital scalp region in non-neurofibromatosis person with diagnosis and management protocol.
منابع مشابه
Intrathoracic Malignant Peripheral Nerve Sheath Tumor: Histopathological and Immunohistochemical Features
Malignant peripheral nerve sheath tumor (MPNST) is a rare nerve sheath tumor derived from Schwann cells or pleuripotent cells of neural crest. Neurogenic tumors make about 10-20% of all mediastinal tumors. Incidence of MPNST is 0.001% in general population and 0.16% in patients with neurofibromatosis I (NF I). We report a case of 60 year female presenting with progressive cough and breathlessne...
متن کاملPrimary Intracranial Malignant Nerve Sheath Tumor in the Cerebellopontine Angle in a Woman with Neurofibromatosis Type 2
Neurofibromatosis type 2 is an inherited disease. The main manifestation of the disease is the development of symmetric, non-malignant brain tumors in the region of the cranial nerve VIII usually as schwannoma. We report here a 20-year-old woman with primary intracranial malignant nerve sheath tumor located in the left cerebellopontine angle. Histologically, the tumor showed malignant spindle c...
متن کاملMalignant Peripheral Nerve Sheath Tumor in the Maxilla: Report of a Rare Case
Malignant peripheral nerve sheath tumor (MPNST) is a rare malignant tumor that develops either from a preexisting neurofibroma or de novo. The cell of origin is believed to be the Schwann cell and possibly other nerve sheath cells. In this report, we describe a rare case of MPNST that arise from the socket of second left maxillary molar that has been already extracted in a young man. He was ref...
متن کاملGiant malignant peripheral nerve sheath tumor of the scalp.
PURPOSE Malignant peripheral nerve sheath tumors (MPNST) constitute a group of soft tissue neoplasms with neurogenic origin. Association of MPNST with neurofibromatosis type 1 (NF1) has been frequently reported as a result of malignant transformation of a pre-existing plexiform neurofibroma. However, most of the cases are small and few have been described with giant dimensions. We describe a ca...
متن کاملMalignant Peripheral Nerve Sheath Tumor of the Inguinum and Angiosarcoma of the Scalp in a Child with Neurofibromatosis Type 1
Benign and malignant tumors are common in the setting of neurofibromatosis type 1 (NF1). Malignant peripheral nerve sheath tumor (MPNST) and angiosarcoma are rare tumors in children and adolescents and mostly occur in young patients in relation to NF1. Both histological types can be present in the same tumor mass in patients with NF1. We present a case of 12.5-year-old girl with NF1 who first p...
متن کامل